Impaired proteoglycan glycosylation, elevated TGF-β signaling, and abnormal osteoblast differentiation as the basis for bone fragility in a mouse model for gerodermia osteodysplastica
Articolo
Data di Pubblicazione:
2018
Tipologia CRIS:
1.1 Articolo in rivista
Keywords:
Animals; Bone Diseases; Cell Differentiation; Decorin; Dermatan Sulfate; Disease Models, Animal; Dwarfism; Female; Fractures, Bone; Glycosylation; Mesenchymal Stem Cells; Mice, Inbred C57BL; Mice, Transgenic; Osteoblasts; Proteoglycans; Signal Transduction; Skin Diseases, Genetic; Transforming Growth Factor beta; Vesicular Transport Proteins; Ecology, Evolution, Behavior and Systematics; Molecular Biology; Genetics; Genetics (clinical); Cancer Research
Elenco autori:
Chan, Wing Lee; Steiner, Magdalena; Witkos, Tomasz; Egerer, Johannes; Busse, Björn; Mizumoto, Shuji; Pestka, Jan M.; Zhang, Haikuo; Hausser, Ingrid; Khayal, Layal Abo; Ott, Claus-Eric; Kolanczyk, Mateusz; Willie, Bettina; Schinke, Thorsten; Paganini, Chiara; Rossi, Antonio; Sugahara, Kazuyuki; Amling, Michael; Knaus, Petra; Chan, Danny; Lowe, Martin; Mundlos, Stefan; Kornak, Uwe
Link alla scheda completa:
Pubblicato in: