Developmental profile of the aberrant dopamine D2 receptor response in striatal cholinergic interneurons in DYT1 dystonia
Articolo
Data di Pubblicazione:
2011
Abstract:
DYT1 dystonia, a severe form of genetically determined human dystonia, exhibits reduced penetrance among carriers and begins usually during adolescence. The reasons for such age dependence and variability remain unclear.
Tipologia CRIS:
1.1 Articolo in rivista
Keywords:
Animals; Receptor; Adenosine A2A; Calcium; GTP-Binding Protein alpha Subunits; Gi-Go; Humans; Dystonia; Mice; Interneurons; Receptors; Dopamine D2; Neostriatum; Electrophysiological Processes; Acetylcholine; Molecular Chaperones; Mutation; Signal Transduction
Elenco autori:
Sciamanna, Giuseppe; Tassone, A; Martella, Giuseppina; Mandolesi, G; Puglisi, F; Cuomo, D; Madeo, Graziella; Ponterio, G; Standaert, D; Bonsi, P; Pisani, Antonio
Link alla scheda completa:
Pubblicato in: