Amyloid fibrils containing fragmented ATTR may be the standard fibril composition in ATTR amyloidosis
Articolo
Data di Pubblicazione:
2013
Tipologia CRIS:
1.1 Articolo in rivista
Keywords:
Familial amyloidotic polyneuropathy; Fibril composition; Transthyretin; TTR non-V30M; TTRV30M; TTRY114C; Adipose Tissue; Adult; Amyloid; Amyloidosis, Familial; Asian Continental Ancestry Group; Cardiomyopathies; European Continental Ancestry Group; Female; Gene Expression; Humans; Male; Middle Aged; Mutation; Myocardium; Peptide Fragments; Phenotype; Prealbumin; Internal Medicine
Elenco autori:
Ihse, Elisabet; Rapezzi, Claudio; Merlini, Giampaolo; Benson, Merrill D.; Ando, Yukio; Suhr, Ole B.; Ikeda, Shu Ichi; Lavatelli, Francesca; Obici, Laura; Quarta, Candida C.; Leone, Ornella; Jono, Hirofumi; Ueda, Mitsuharu; Lorenzini, Massimiliano; Liepnieks, Juris; Ohshima, Toshinori; Tasaki, Masayoshi; Yamashita, Taro; Westermark, Per
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